The spectrum of inflammatory bowel diseases includes ulcerative colitis, Crohn's disease and unclassified inflammatory bowel disease. It is an idiopathic, chronic inflammatory disease that affects the digestive system with frequent extraintestinal manifestations. The incidence of IBD is increasing globally. Despite numerous studies, the etiopathogenesis is still not fully understood. According to current knowledge, chronic intestinal inflammation is the result of the interaction between the genetic predisposition of the host, the intestinal microbiota, external environmental factors and an abnormal immune response. Extraintestinal manifestations of IBD occur in 25% to 40% of patients and most commonly affect the musculoskeletal system, skin, hepatobiliary tract and eyes. Based on the pathogenesis, the dermatological manifestations of IBD can be divided into 4 categories: 1) dermatological manifestations with the same histological features of underlying IBD, 2) reactive manifestations of IBD due to immunological response to common antigens shared by gut bacteria and skin, 3) mucocutaneus manifestations associated with IBD, 4) skin disorders or dermatoses associated with IBD. The most common dermatological manifestations of inflammatory bowel disease are erythema nodosum, pyoderma gangrenosum and aphthous stomatitis. Sweet's syndrome, bowel-associated dermatosis-arthritis syndrome, metastatic Crohn's disease and acquired epidermolysis bullosa occur less frequently. Some skin manifestations are directly related to the activity of the underlying disease and adequate treatment of IBD leads to regression of skin changes. Skin manifestations that are independent of IBD require multidisciplinary team and additional therapy.