prikaz prve stranice dokumenta Consensus recommendations from the EXPeRT/PARTNER groups for the diagnosis and therapy of sex cord stromal tumors in children and adolescents
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Consensus recommendations from the EXPeRT/PARTNER groups for the diagnosis and therapy of sex cord stromal tumors in children and adolescents
Pediatric Blood & Cancer, (2021); 29017. https://doi.org/10.1002/pbc.29017
Schneider, Dominik T.; Orbach, Daniel; Ben‐Ami, Tal; Bien, Ewa; Bisogno, Gianni; Brecht, Ines B.; Cecchetto, Giovanni; Ferrari, Andrea; Godzinski, Jan; Janic, Dragana; Lopez Almaraz, Ricardo; Pourtsidis, Apostolos; Roganovic, Jelena; Schultz, Kris Ann P.; Stachowicz‐Stencel, Teresa; Fresneau, Brice More authors...

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Schneider, D. T., Orbach, D., Ben‐Ami, T., Bien, E., Bisogno, G., Brecht, I. B. ... Fresneau, B. (2021). Consensus recommendations from the EXPeRT/PARTNER groups for the diagnosis and therapy of sex cord stromal tumors in children and adolescents. Pediatric Blood & Cancer. doi: 10.1002/pbc.29017

Schneider, Dominik T., et al. "Consensus recommendations from the EXPeRT/PARTNER groups for the diagnosis and therapy of sex cord stromal tumors in children and adolescents." Pediatric Blood & Cancer, 2021. https://doi.org/10.1002/pbc.29017

Schneider, Dominik T., Daniel Orbach, Tal Ben‐Ami, Ewa Bien, Gianni Bisogno, Ines B. Brecht, Giovanni Cecchetto, et al. "Consensus recommendations from the EXPeRT/PARTNER groups for the diagnosis and therapy of sex cord stromal tumors in children and adolescents." Pediatric Blood & Cancer (2021). https://doi.org/10.1002/pbc.29017

Schneider, D. T., et al. (2021) 'Consensus recommendations from the EXPeRT/PARTNER groups for the diagnosis and therapy of sex cord stromal tumors in children and adolescents', Pediatric Blood & Cancer. doi: 10.1002/pbc.29017

Schneider DT, Orbach D, Ben‐Ami T, Bien E, Bisogno G, Brecht IB, and sur.. Consensus recommendations from the EXPeRT/PARTNER groups for the diagnosis and therapy of sex cord stromal tumors in children and adolescents. Pediatric Blood & Cancer [Internet]. 2021 March 24 [cited 2024 December 02]. doi: 10.1002/pbc.29017

D. T. Schneider, et al., "Consensus recommendations from the EXPeRT/PARTNER groups for the diagnosis and therapy of sex cord stromal tumors in children and adolescents", Pediatric Blood & Cancer, March 2021. [Online]. Available at: https://urn.nsk.hr/urn:nbn:hr:184:578028. [Accessed: 02 December 2024]

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Metadata
Title (english)Consensus recommendations from the EXPeRT/PARTNER groups for the diagnosis and therapy of sex cord stromal tumors in children and adolescents
AuthorDominik T. Schneider
AuthorDaniel Orbach
AuthorTal Ben‐Ami
AuthorEwa Bien
AuthorGianni Bisogno
AuthorInes B. Brecht
AuthorGiovanni Cecchetto
AuthorAndrea Ferrari
AuthorJan Godzinski
AuthorDragana Janic
AuthorRicardo Lopez Almaraz
AuthorApostolos Pourtsidis
AuthorJelena Roganovic
AuthorKris Ann P. Schultz
AuthorTeresa Stachowicz‐Stencel
AuthorBrice Fresneau
Author's institutionUniversity of Rijeka
Faculty of Medicine
(Department of Pediatrics)
Scientific / art field,
discipline and subdiscipline		BIOMEDICINE AND HEALTHCARE
Clinical Medical Sciences
Abstract (english)
As part of the European Union-funded project designated Paediatric Rare Tumours Network - European Registry (PARTNER), the European Cooperative Study Group for Pediatric Rare Tumors (EXPeRT) is continuously developing consensus recommendations in order to harmonize standard care for very rare solid tumors of children and adolescents. This paper presents the internationally recognized recommendations for the diagnosis and treatment of sex cord stromal tumors (SCST). The clinical approach to sex cord stromal tumors of the testis (TSCST) and ovary (OSCST) depends on histological differentiation and tumor stage. Virtually all TSCSTs present as localized nonmetastatic tumors, with excellent prognosis after complete resection. In contrast, the prognosis of OSCSTs may be adversely affected by tumor spillage during surgery or presence of metastases. In these cases, cisplatin-based chemotherapy is recommended. Of note, some SCSTs may develop in the context of tumor predisposition syndromes, for example, DICER-1, so that specific follow-up is indicated. SCSTs should be diagnosed and treated according to standardized recommendations that include reference pathology, genetic testing for tumor predisposition syndromes in selected cases, and stratified adjuvant chemotherapy in patients with unfavorable risk profile. To ensure high quality of diagnosis and therapy, patients should be enrolled into prospective registries.
Keywords (english)
Languageenglish
Publication typeProfessional paper - Professional paper
Publication statusAccepted
Peer reviewPeer review - international
Publication versionPublished version
Journal titlePediatric Blood & Cancer
Numbering29017
p-ISSN1545-5009
e-ISSN1545-5017
DOIhttps://doi.org/10.1002/pbc.29017
URN:NBNurn:nbn:hr:184:578028
Publication2021-03-24
Document URLhttps://onlinelibrary.wiley.com/doi/10.1002/pbc.29017
Type of resourceText
Access conditionsRestricted access
Terms of useLicence In copyright icon
Created on2021-04-14 13:36:13